Multidisciplinary Approach for Dental Management of Pediatric Patient with DiGeorge Syndrome and Tetralogy of Fallot: A Case Report

Autores

  • Nilton José da Silva Filho MS, Oral and Maxillofacial Surgery Department of the Campo Limpo Municipal Hospital, São Paulo, Brazil https://orcid.org/0000-0001-5802-8362
  • Sthefanne Gondim Mota DDS, Oral and Maxillofacial Surgery Department of the Campo Limpo Municipal Hospital, São Paulo, Brazil https://orcid.org/0000-0001-5759-5787
  • Amy Brian Costa e Silva DDS, Oral and Maxillofacial Surgery Department of the Campo Limpo Municipal Hospital, São Paulo, Brazil
  • Ian Artoni de Oliveira Silva School of Dentistry, University of São Paulo (USP), São Paulo, Brazil; Oral and Maxillofacial Surgery Department of the Campo Limpo Municipal Hospital, São Paulo, Brazil https://orcid.org/0009-0000-1496-0342
  • Thaynara Gomes Rodrigues School of Dentistry, University of São Paulo (USP), São Paulo, Brazil; Oral and Maxillofacial Surgery Department of the Campo Limpo Municipal Hospital, São Paulo, Brazil https://orcid.org/0009-0004-7601-0747
  • João Alves Gonçalves Neto MS, Piracicaba School of Dentistry, University of Campinas https://orcid.org/0009-0001-4262-0211
  • Leandro Curvello Teixeira DDS, Oral and Maxillofacial Surgery Department of the Campo Limpo Municipal Hospital, São Paulo, Brazil https://orcid.org/0009-0006-7274-3382
  • Talita Lopes MSC, Oral and Maxillofacial Surgery Department of the Campo Limpo Municipal Hospital, São Paulo, Brazil https://orcid.org/0000-0001-8881-7944
  • Basilio de Almeida Milani MS, Oral and Maxillofacial Surgery Department of the Campo Limpo Municipal Hospital, São Paulo, Brazil
  • Diego Girotto Bussaneli PhD, Araraquara Dental School, São Paulo State University, Araraquara - Brazil https://orcid.org/0000-0001-9078-7385

DOI:

https://doi.org/10.21270/archi.v14i12.6656

Palavras-chave:

Pediatric Dentistry, Tetralogy of Fallot, Digeorge Syndrome, Heart Defects, Congenital

Resumo

Patients with congenital heart disease (CHD), particularly those with associated syndromes such as DiGeorge Syndrome (DGS), present unique challenges in dental management due to systemic and oral health complexities. DGS is a genetic condition that affects multiple systems, including craniofacial and dental structures, often leading to enamel defects and an increased risk of dental caries. Tetralogy of Fallot (ToF), a common CHD, further compounds these challenges due to the heightened risk of bacterial endocarditis associated with oral infections. This case report details the dental management of a 7-year-old boy with both DGS and repaired ToF. The patient was presented with severe dental caries, poor oral hygiene, and non-collaborative behavior, necessitating treatment under general anesthesia. A multidisciplinary team, including cardiologists, anesthesiologists, and oral surgeons, coordinated care to ensure a safe and effective approach. Multiple extractions were performed under antibiotic prophylaxis to minimize the risk of infection and systemic complications. Post-operative recovery was uneventful, and follow-up revealed satisfactory healing and improved oral care adherence. This report highlights the importance of a multidisciplinary strategy in managing dental treatment for medically complex pediatric patients. Early diagnosis, preventive measures, and collaboration among healthcare providers are crucial to optimizing oral and systemic health outcomes while minimizing risks.

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Publicado

2025-12-31

Como Citar

Silva Filho, N. J. da, Mota, S. G., Silva, A. B. C. e, Silva, I. A. de O., Rodrigues, T. G., Gonçalves Neto, J. A., … Bussaneli, D. G. (2025). Multidisciplinary Approach for Dental Management of Pediatric Patient with DiGeorge Syndrome and Tetralogy of Fallot: A Case Report. ARCHIVES OF HEALTH INVESTIGATION, 14(12), 2733–2738. https://doi.org/10.21270/archi.v14i12.6656

Edição

v. 14 n. 12 (2025)

Seção

Original Articles