Abordaje Multidisciplinario para el Manejo Dental de un Paciente Pediátrico con Síndrome de DiGeorge y Tetralogía de Fallot: Reporte de un Caso

Autores/as

  • Nilton José da Silva Filho MS, Oral and Maxillofacial Surgery Department of the Campo Limpo Municipal Hospital, São Paulo, Brazil https://orcid.org/0000-0001-5802-8362
  • Sthefanne Gondim Mota DDS, Oral and Maxillofacial Surgery Department of the Campo Limpo Municipal Hospital, São Paulo, Brazil https://orcid.org/0000-0001-5759-5787
  • Amy Brian Costa e Silva DDS, Oral and Maxillofacial Surgery Department of the Campo Limpo Municipal Hospital, São Paulo, Brazil
  • Ian Artoni de Oliveira Silva School of Dentistry, University of São Paulo (USP), São Paulo, Brazil; Oral and Maxillofacial Surgery Department of the Campo Limpo Municipal Hospital, São Paulo, Brazil https://orcid.org/0009-0000-1496-0342
  • Thaynara Gomes Rodrigues School of Dentistry, University of São Paulo (USP), São Paulo, Brazil; Oral and Maxillofacial Surgery Department of the Campo Limpo Municipal Hospital, São Paulo, Brazil https://orcid.org/0009-0004-7601-0747
  • João Alves Gonçalves Neto MS, Piracicaba School of Dentistry, University of Campinas https://orcid.org/0009-0001-4262-0211
  • Leandro Curvello Teixeira DDS, Oral and Maxillofacial Surgery Department of the Campo Limpo Municipal Hospital, São Paulo, Brazil https://orcid.org/0009-0006-7274-3382
  • Talita Lopes MSC, Oral and Maxillofacial Surgery Department of the Campo Limpo Municipal Hospital, São Paulo, Brazil https://orcid.org/0000-0001-8881-7944
  • Basilio de Almeida Milani MS, Oral and Maxillofacial Surgery Department of the Campo Limpo Municipal Hospital, São Paulo, Brazil
  • Diego Girotto Bussaneli PhD, Araraquara Dental School, São Paulo State University, Araraquara - Brazil https://orcid.org/0000-0001-9078-7385

DOI:

https://doi.org/10.21270/archi.v14i12.6656

Palabras clave:

Odontología Pediátrica, Tetralogía de Fallot, Síndrome de DiGeorge, Cardiopatías Congénitas

Resumen

Los pacientes con cardiopatías congénitas (CHD, por sus siglas en inglés), particularmente aquellos con síndromes asociados como el síndrome de DiGeorge (DGS), presentan desafíos únicos en el manejo odontológico debido a las complejidades de la salud sistémica y oral. El DGS es una condición genética que afecta múltiples sistemas, incluyendo las estructuras craneofaciales y dentales, lo que a menudo conduce a defectos del esmalte y a un mayor riesgo de caries dental. La Tetralogía de Fallot (ToF), una CHD común, agrava aún más estos desafíos debido al mayor riesgo de endocarditis bacteriana asociada con infecciones orales. Este informe de caso detalla el manejo odontológico de un niño de 7 años con DGS y ToF reparada. El paciente presentaba caries dentales severas, mala higiene oral y un comportamiento poco colaborativo, lo que requirió tratamiento bajo anestesia general. Un equipo multidisciplinario, que incluía cardiólogos, anestesiólogos y cirujanos orales, coordinó la atención para garantizar un enfoque seguro y eficaz. Se realizaron múltiples extracciones bajo profilaxis antibiótica para minimizar el riesgo de infección y complicaciones sistémicas. La recuperación postoperatoria fue sin incidentes, y el seguimiento mostró una cicatrización satisfactoria y una mejor adherencia al cuidado oral. Este informe destaca la importancia de una estrategia multidisciplinaria en el manejo del tratamiento odontológico para pacientes pediátricos médicamente complejos. El diagnóstico temprano, las medidas preventivas y la colaboración entre los proveedores de atención médica son fundamentales para optimizar los resultados en la salud oral y sistémica mientras se minimizan los riesgos.

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Publicado

2025-12-31

Cómo citar

Silva Filho, N. J. da, Mota, S. G., Silva, A. B. C. e, Silva, I. A. de O., Rodrigues, T. G., Gonçalves Neto, J. A., … Bussaneli, D. G. (2025). Abordaje Multidisciplinario para el Manejo Dental de un Paciente Pediátrico con Síndrome de DiGeorge y Tetralogía de Fallot: Reporte de un Caso. ARCHIVES OF HEALTH INVESTIGATION, 14(12), 2733–2738. https://doi.org/10.21270/archi.v14i12.6656

Número

Vol. 14 Núm. 12 (2025)

Sección

Original Articles